666
Views & Citations10
Likes & Shares
Introduction: The
peripheral primitive neuroectodermal tumor (PNET) is a malignant small round
cell neoplasm of neural origin that arises outside the brain, spinal cord and
sympathetic nervous system. This tumor most often arises in the chest wall and
paraspinal region; however, less common origins have been described in
literature including bones, limbs and genitourinary tract. We here report one
case of primitive neuroectodermal tumor of kidney in our Institution.
Case report: A 23
year old male presented with complaints of pain abdomen and fever since a week.
There was no history of hematuria, vomiting or burning micturition. On
examination, right renal angle tenderness was present; a vague mass was
palpable in right lumbar region. Ultrasonography showed lobulated hypoechoic
lesion in lower pole of right kidney. CT scans revealed, well defined
heterogeneously enhancing iso- to hypo-dense lesion measuring 5 × 4.6 × 4.6 cm
in lower pole of right kidney. On post contrast study, lesion shows
heterogenous enhancement with multiple non enhancing areas within-s/o necrosis.
Patient underwent nephrectomy. Histopathology revealed round cell tumor with
capsular, perinephric fat and lymphovascular invasion. Renal sinus showed tumor
infiltration. Immunohistochemically neuron specific marker was identified.
Conclusion: PNET
is extremely rare in the kidney, but because of its imaging characteristics,
when a large necrotic and hemorrhagic renal mass is found in within the tumor
are less likely to indicate this diagnosis. Exact diagnosis of PNET of kidney
should be done using immunohistochemical markers.
QUICK LINKS
- SUBMIT MANUSCRIPT
- RECOMMEND THE JOURNAL
-
SUBSCRIBE FOR ALERTS
RELATED JOURNALS
- International Journal of Surgery and Invasive Procedures (ISSN:2640-0820)
- International Journal of Clinical Case Studies and Reports (ISSN:2641-5771)
- International Journal of Anaesthesia and Research (ISSN:2641-399X)
- Journal of Forensic Research and Criminal Investigation (ISSN: 2640-0846)
- Journal of Spine Diseases
- International Journal of AIDS (ISSN: 2644-3023)
- Stem Cell Research and Therapeutics (ISSN:2474-4646)